Cryptotia

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Cryptotia
Other namesFamilial cryptotia [1]
Autosomal dominant - en.svg
This condition is inherited in an autosomal dominant manner

Cryptotia is the condition where an ear appears to have its upper portion buried underneath the side of the head. The condition also involves underdeveloped scapha and antihelical crura. Cryptotia is also known as buried ear or hidden ear. [2]

Contents

Signs and symptoms

The invagination of the upper portion of the auricle beneath the auricular cartilage deformity is one of the most prevalent characteristics of cryptotia. [3]

Diagnosis

Based on the kind of antihelix deformity and the condition of the intrinsic auricular muscle, there are two types of cryptotia. Type I cryptotia is characterized by compression of the antihelix's body and superior crus, burying the upper portion beneath the skin. The inferior crus of the antihelix is severely bent over in type II cryptotia, and the antihelix's body has contracted grossly. [3]

Treatment

Cryptotia is often treated through surgery which involves releasing the ear from its buried position, reshaping the cartilage and using local tissue to resurface the released cartilage. [4]

Epidemiology

Cryptotia is common amongst Asians but rare in Europeans. [5] Based on studies the incident of cryptotia in Japan is about 1 in every 400 births. [6]

See also

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References

  1. "OMIM Entry - 123557 - CRYPTOTIA, FAMILIAL". omim.org. Retrieved 30 March 2019.
  2. Bray, David Jr. "Cryptotia" . Retrieved December 28, 2011.
  3. 1 2 Hirose, Takeshi; Tomono, Tokio; Matsuo, Kiyoshi; Katohda, Susumu; Takahashi, Nobuyuki; Iwasaw, Motonao; Satoh, Reiko (1985). "Cryptotia: our classification and treatment". British Journal of Plastic Surgery. 38 (3). Elsevier BV: 352–360. doi:10.1016/0007-1226(85)90241-3. ISSN   0007-1226. PMID   4016423.
  4. University of North Carolina, Chapel Hill, School of Medicine. "Cryptotia". Archived from the original on April 7, 2012. Retrieved December 28, 2011.{{cite web}}: CS1 maint: multiple names: authors list (link)
  5. Kim, Seok-Kwun; Yoon, Chung-Min; Kim, Myung-Hoon; Kim, Min-Su; Lee, Keun-Cheol (2012). "Considerations for the Management of Cryptotia Based on the Experience of 34 Patients". Archives of Plastic Surgery. 39 (6). Georg Thieme Verlag KG: 601–605. doi:10.5999/aps.2012.39.6.601. ISSN   2234-6163. PMID   23233884.
  6. OHMORI, SEIICHI; MATSUMOTO, KOREAKI (1972). "Treatment of Cryptotia, Using Teflon String". Plastic and Reconstructive Surgery. 49 (1). Ovid Technologies (Wolters Kluwer Health): 33–37. doi:10.1097/00006534-197201000-00006. ISSN   0032-1052. PMID   4550069. S2CID   33854591.

Further reading