Blake Croll Papsin, FACS (born 1959) [1] is a Canadian [2] otolaryngologist who has worked at the Hospital for Sick Children since 1996. Following his graduation from the University of Toronto Faculty of Medicine, he worked at Mount Sinai Hospital as an associate professor, [1] and following surgical training in cochlear implants, he became known for implantation of those techniques. [3] [4] In 2014 he led the team that discovered that putting infants too close to an improperly used white noise machine could put infants at a high risk of developing hearing loss. [2] [5] [6] [7]
Hearing loss is a partial or total inability to hear. Hearing loss may be present at birth or acquired at any time afterwards. Hearing loss may occur in one or both ears. In children, hearing problems can affect the ability to acquire spoken language, and in adults it can create difficulties with social interaction and at work. Hearing loss can be temporary or permanent. Hearing loss related to age usually affects both ears and is due to cochlear hair cell loss. In some people, particularly older people, hearing loss can result in loneliness.
Sudden infant death syndrome (SIDS), sometimes known as cot death, is the sudden unexplained death of a child of less than one year of age. Diagnosis requires that the death remain unexplained even after a thorough autopsy and detailed death scene investigation. SIDS usually occurs during sleep. Typically death occurs between the hours of midnight and 9:00a.m. There is usually no noise or evidence of struggle. SIDS remains the leading cause of infant mortality in Western countries, constituting half of all post-neonatal deaths.
A cochlear implant (CI) is a surgically implanted neuroprosthesis that provides a person who has moderate-to-profound sensorineural hearing loss with sound perception. With the help of therapy, cochlear implants may allow for improved speech understanding in both quiet and noisy environments. A CI bypasses acoustic hearing by direct electrical stimulation of the auditory nerve. Through everyday listening and auditory training, cochlear implants allow both children and adults to learn to interpret those signals as speech and sound.
Auditory neuropathy (AN) is a hearing disorder in which the outer hair cells of the cochlea are present and functional, but sound information is not transmitted sufficiently by the auditory nerve to the brain. The cause may be several dysfunctions of the inner hair cells of the cochlea or spiral ganglion neuron levels. Hearing loss with AN can range from normal hearing sensitivity to profound hearing loss.
Unilateral hearing loss (UHL) is a type of hearing impairment where there is normal hearing in one ear and impaired hearing in the other ear.
Presbycusis, or age-related hearing loss, is the cumulative effect of aging on hearing. It is a progressive and irreversible bilateral symmetrical age-related sensorineural hearing loss resulting from degeneration of the cochlea or associated structures of the inner ear or auditory nerves. The hearing loss is most marked at higher frequencies. Hearing loss that accumulates with age but is caused by factors other than normal aging is not presbycusis, although differentiating the individual effects of distinct causes of hearing loss can be difficult.
Graeme Milbourne Clark is an Australian Professor of Otolaryngology at the University of Melbourne. Worked in ENT surgery, electronics and speech science contributed towards the development of the multiple-channel cochlear implant. His invention was later marketed by Cochlear Limited.
A bone-anchored hearing aid (BAHA) is a type of hearing aid based on bone conduction. It is primarily suited for people who have conductive hearing losses, unilateral hearing loss, single-sided deafness and people with mixed hearing losses who cannot otherwise wear 'in the ear' or 'behind the ear' hearing aids. They are more expensive than conventional hearing aids, and their placement involves invasive surgery which carries a risk of complications, although when complications do occur, they are usually minor.
The auditory brainstem response (ABR), also called brainstem evoked response audiometry (BERA) or brainstem auditory evoked potentials (BAEPs) or brainstem auditory evoked responses (BAERs) is an auditory evoked potential extracted from ongoing electrical activity in the brain and recorded via electrodes placed on the scalp. The measured recording is a series of six to seven vertex positive waves of which I through V are evaluated. These waves, labeled with Roman numerals in Jewett and Williston convention, occur in the first 10 milliseconds after onset of an auditory stimulus. The ABR is considered an exogenous response because it is dependent upon external factors.
Ramesh C. Deka is an Indian Ear, Nose and Throat (ENT) specialist and the former Director of All India Institute of Medical Sciences, New Delhi, which is globally recognised as the premier medical institute of India. He is one of the pioneers of cochlear implant surgery in India and performed the country's first bilateral cochlear implantation surgery.
Prelingual deafness refers to deafness that occurs before learning speech or language. Speech and language typically begin to develop very early with infants saying their first words by age one. Therefore, prelingual deafness is considered to occur before the age of one, where a baby is either born deaf or loses hearing before the age of one. This hearing loss may occur for a variety of reasons and impacts cognitive, social, and language development.
Language acquisition is a natural process in which infants and children develop proficiency in the first language or languages that they are exposed to. The process of language acquisition is varied among deaf children. Deaf children born to deaf parents are typically exposed to a sign language at birth and their language acquisition follows a typical developmental timeline. However, at least 90% of deaf children are born to hearing parents who use a spoken language at home. Hearing loss prevents many deaf children from hearing spoken language to the degree necessary for language acquisition. For many deaf children, language acquisition is delayed until the time that they are exposed to a sign language or until they begin using amplification devices such as hearing aids or cochlear implants. Deaf children who experience delayed language acquisition, sometimes called language deprivation, are at risk for lower language and cognitive outcomes. However, profoundly deaf children who receive cochlear implants and auditory habilitation early in life often achieve expressive and receptive language skills within the norms of their hearing peers; age at implantation is strongly and positively correlated with speech recognition ability. Early access to language through signed language or technology have both been shown to prepare children who are deaf to achieve fluency in literacy skills.
Blake Shaw Wilson is an American research scientist best known for his role in developing signal processing strategies for the cochlear implant.
The Bionics Institute is an Australian medical research institute focusing on medical device development. It is located in Melbourne, Australia.
Language exposure for children is the act of making language readily available and accessible during the critical period for language acquisition. Deaf and hard of hearing children, when compared to their hearing peers, tend to face more hardships when it comes to ensuring that they will receive accessible language during their formative years. Therefore, deaf and hard of hearing children are more likely to have language deprivation which causes cognitive delays. Early exposure to language enables the brain to fully develop cognitive and linguistic skills as well as language fluency and comprehension later in life. Hearing parents of deaf and hard of hearing children face unique barriers when it comes to providing language exposure for their children. Yet, there is a lot of research, advice, and services available to those parents of deaf and hard of hearing children who may not know how to start in providing language.
Temporal envelope (ENV) and temporal fine structure (TFS) are changes in the amplitude and frequency of sound perceived by humans over time. These temporal changes are responsible for several aspects of auditory perception, including loudness, pitch and timbre perception and spatial hearing.
Robert V. Shannon is Research Professor of Otolaryngology-Head & Neck Surgery and Affiliated Research Professor of Biomedical Engineering at University of Southern California, CA, USA. Shannon investigates the basic mechanisms underlying auditory neural processing by users of cochlear implants, auditory brainstem implants, and midbrain implants.
Rochelle Newman is an American psychologist. She is chair of the University of Maryland Department of Hearing and Speech Sciences (HESP), as well as associate director of the Maryland Language Science Center. She previously served as the director of graduate studies for both HESP and the Program in Neuroscience and Cognitive Science and is also a member of the Center for the Comparative & Evolutionary Biology of Hearing. Newman helped found the University of Maryland Infant & Child Studies Consortium and the University of Maryland Autism Research Consortium.
Richard Charles Dowell is an Australian audiologist, academic and researcher. He holds the Graeme Clark Chair in Audiology and Speech Science at University of Melbourne. He is a former director of Audiological Services at Royal Victorian Eye and Ear Hospital.
John Oghalai is an American physician and scientist. He is the Leon J. Tiber and David S. Alpert Chair in Medicine at the University of Southern California Keck School of Medicine and chair of the USC Caruso Department of Otolaryngology. Oghalai is an otolaryngologist. His research focuses on anatomical and molecular mechanisms in hearing and in ear and hearing disorders.