Congenital clasped thumb

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Congenital clasped thumb
Other namesinfant’s persistent thumb-clutched hand, [1] flexion-adduction deformity of the thumb, [2] pollex varus, [3] thumb in the hand deformity. [4]
Congenital clasped thumb right.jpg
Congenital clasped thumb

Congenital clasped thumb describes an anomaly which is characterized by a fixed thumb into the palm at the metacarpophalangeal joint in one or both hands. [5] The incidence and genetic background are unknown. A study of Weckesser et al. showed that boys are twice as often affected with congenital clasped thumb compared to girls. The anomaly is in most cases bilateral (present in both hands). [5] A congenital clasped thumb can be an isolated anomaly, but can also be attributed to several syndromes.

Contents

Causes

The thumb contains five groups of muscle and/or tendons:[ citation needed ]

  1. Extensor tendons (to stretch the thumb)
  2. Flexor muscles/tendons (to bend the thumb)
  3. Abductor muscles/tendons (to move the thumb outwards)
  4. Adductor muscle (to move the thumb inwards)
  5. Opposing muscles (to move the thumb opposite the small finger)

In order for the thumb to maintain a normal position, a strict balance between these groups is required. Weak or absent extensors and/or abductors (the extensor pollicis brevis tendon, the extensor pollicis longus tendon or, rarely, the abductor pollicis longus tendon), can cause a disbalance, leading to an abnormal position of the thumb: congenital clasped thumb. There is also the possibility that two tendons are affected simultaneously.[ citation needed ]

The following tendon deviations can induce congenital clasped thumb:

Furthermore, a tight thumb web space (the area between thumb and index finger) can contribute to congenital clasped thumb. The thumb cannot be properly abducted (moved outwards), if the web space is too tight.[ citation needed ]

To summarize, the causes of congenital clasped thumbs may vary between patients and can sometimes be a combination of the preceding components. Treatment should be tailored to all occurring components in order to achieve good results.[ citation needed ]

Diagnosis

Diagnosing the congenital clasped thumb is difficult in the first three to four months of life, as it is normal when the thumb is clutched into the palm in these first months. [6] Diagnoses that cause the same flexion or adduction abnormalities of the thumb are:

Syndrome associated flexion-adduction of the thumb:

Classification

There are a few different classifications conceived to categorize the spectrum of variety of congenital clasped thumb. In literature, X classifications have been described for clasped thumb. The two most relevant of the existing classifications, to our opinion, are the classifications of McCarrol [12] and Tjuyuguchi et al. [13]

The most global format is the classification of McCarrol, which divides the congenital clasped thumbs into two groups. Group I includes the supple clasped thumb, when the thumb is only passively correctable. While complex clasped thumbs, thumbs which cannot be moved neither passively or actively, belong to group II.[ citation needed ]

Tjuyuguchi et al. designed a classification existing of three groups:[ citation needed ]

Treatment

Treatment of congenital clasped thumb includes two types of therapy: conservative and surgical.

Conservative treatment

Treatment of all categories of congenital clasped thumbs should start with either serial plaster casting or wearing a static or dynamic splint for a period of six months, [5] while massaging the hand. Extension by splinting shows reduction of the flexion contracture. To gain optimal results, it is important to start this treatment before the age of six months. The result of this therapy is better in less severe deformities. [14] In most uncomplicated cases, a satisfactory result can be gained when splint therapy starts before the age of six months. [15] Splinting should be tried for at least three months and possibly for as long as six months or longer. If the result of splint therapy stagnates, surgery treatment is indicated. [16]

Surgical treatment

Surgical treatment should be considered in patients who have not been treated at younger age or when conservative therapy fails. Surgery is recommended during the age of three to five years.[ citation needed ]

Techniques

Other procedures

Related Research Articles

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<span class="mw-page-title-main">De Quervain syndrome</span> Restricted movement of tendons controlling the thumb

De Quervain syndrome occurs when two tendons that control movement of the thumb become constricted by their tendon sheath in the wrist. This results in pain and tenderness on the thumb side of the wrist. Radial abduction of the thumb is painful. On some occasions, there is uneven movement or triggering of the thumb with radial abduction. Symptoms can come on gradually or be noted suddenly.

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<span class="mw-page-title-main">Arthrogryposis</span> Medical condition

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<span class="mw-page-title-main">Dorsal interossei of the hand</span> Muscles between the metacarpals

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<span class="mw-page-title-main">Muscles of the hand</span> Muscles of the human hand

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<span class="mw-page-title-main">Ulnar claw</span> Deformity of the hand that develops due to ulnar nerve damage

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<span class="mw-page-title-main">Swan neck deformity</span> Medical condition

Swan neck deformity is a deformed position of the finger, in which the joint closest to the fingertip is permanently bent toward the palm while the nearest joint to the palm is bent away from it. It is commonly caused by injury, hypermobility or inflammatory conditions like rheumatoid arthritis or sometimes familial.

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<span class="mw-page-title-main">Median nerve palsy</span> Medical condition

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<span class="mw-page-title-main">Congenital trigger thumb</span> Medical condition

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<span class="mw-page-title-main">Radial dysplasia</span> Medical condition

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