Ross' syndrome

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Ross' syndrome
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Ross' syndrome consists of Adie's syndrome (myotonic pupils and absent deep tendon reflexes) plus segmental anhidrosis (typically associated with compensatory hyperhidrosis). [1]

Contents

It was characterized in 1958 [2] [3] by A. T. Ross. [4]

By 1992, eighteen cases had been documented. [5]

Signs and symptoms

Initial manifestations often include an abnormal segmental sweating response (described as hyperhidrosis or anhidrosis in some patients) and a tonic pupil. Other commonly reported symptoms included fatigue, chronic cough, and increased urinary frequency. [6]

Prognosis

Ross syndrome is a non life-threatening benign condition but delay in diagnosis can result in slow progression of autonomic symptoms. [7]

Epidemiology

Ross Syndrome is a progressive autonomic dysfunction that can occur in any age, ethnicity, or gender. The average age of diagnosis for Ross syndrome is 36 years and affects more females than males. [7]

See also

References

  1. ↑ Bolognia JL, Jorizzo JL, Rapini RP, eds. (2007). Dermatology: 2-Volume Set (2nd ed.). St. Louis: Mosby. p. 539. ISBN   978-1-4160-2999-1.
  2. ↑ Otto Braun-Falco (2000). Dermatology. Springer. pp. 1093–. ISBN   978-3-540-59452-9 . Retrieved 20 November 2010.
  3. ↑ Yaşar S, Aslan C, Serdar ZA, Demirci GT, Tutkavul K, Babalik D (April 2010). "Ross syndrome: Unilateral hyperhidrosis, Adie's tonic pupils and diffuse areflexia". J Dtsch Dermatol Ges. 8 (12): 1004–1006. doi:10.1111/j.1610-0387.2010.07400.x. PMID   20408939. S2CID   24213039.
  4. ↑ Ross AT (November 1958). "Progressive selective sudomotor denervation; a case with coexisting Adie's syndrome". Neurology. 8 (11): 809–17. doi:10.1212/wnl.8.11.809. PMID   13590391. S2CID   2610900.
  5. ↑ Weller M, Wilhelm H, Sommer N, Dichgans J, Wiethölter H (April 1992). "Tonic pupil, areflexia, and segmental anhidrosis: two additional cases of Ross syndrome and review of the literature". J. Neurol. 239 (4): 231–4. doi:10.1007/BF00839146. PMID   1597691. S2CID   8832477.
  6. ↑ Lamotte, Guillaume; Sandroni, Paola; Cutsforth-Gregory, Jeremy K.; Berini, Sarah E.; Benarroch, Eduardo E.; Shouman, Kamal; Mauermann, Michelle L.; Anderson, Jennifer; Low, Phillip A.; Singer, Wolfgang; Coon, Elizabeth A. (2021-10-01). "Clinical presentation and autonomic profile in Ross syndrome". Journal of Neurology. 268 (10): 3852–3860. doi:10.1007/s00415-021-10531-8. ISSN   1432-1459. PMC   9639164 . PMID   33813643.
  7. 1 2 "Ross syndrome | DermNet NZ". dermnetnz.org. Retrieved 2021-12-07.
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