Onychogryphosis

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Onychogryposis
Other namesOnychogryposis or Ram's horn nails [1]
ONYCHOGRYPHOSIS1.JPG
Specialty Dermatology   OOjs UI icon edit-ltr-progressive.svg

Onychogryphosis is a hypertrophy that may produce nails resembling claws or a ram's horn.

Contents

Causes

Onychogryphosis demonstrating the characteristic ram's horn appearance Onychogryphosis (2).jpg
Onychogryphosis demonstrating the characteristic ram's horn appearance
Ram's horn toenails on a bedridden patient Ram's horn toenails on a bedridden patient.jpg
Ram's horn toenails on a bedridden patient

Onychogryphosis may be caused by trauma or peripheral vascular disease, but most often secondary to self-neglect and failure to cut the nails for extended periods of time. [2] :783–4 [3] This condition is most commonly seen in the elderly. [4]

Treatment

Some recommend avulsion of the nail plate with surgical destruction of the nail matrix with phenol or the carbon dioxide laser, if the blood supply is adequate. [2] :783–4 [5] :659

Epidemiology

Severe congenital onychogryphosis affecting all twenty nailbeds has been recorded in two families who exhibit the dominant allele for a certain gene. [6] [7]

Congenital onychogryphosis of the fifth toe (the baby, little, pinky or small toe) is fairly common, but asymptomatic and seldom brought to the attention of medical professionals. Rather, it is brought to the attention of manicurists who routinely file the clawed toenail flat.

See also

Related Research Articles

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A nail disease or onychosis is a disease or deformity of the nail. Although the nail is a structure produced by the skin and is a skin appendage, nail diseases have a distinct classification as they have their own signs and symptoms which may relate to other medical conditions. Some nail conditions that show signs of infection or inflammation may require medical assistance.

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Paronychia is an inflammation of the skin around the nail, which can occur suddenly, when it is usually due to the bacterium Staphylococcus aureus, or gradually when it is commonly caused by the fungus Candida albicans. The term is from Greek: παρωνυχία from para 'around', onyx 'nail', and the abstract noun suffix -ia.

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Acral fibrokeratoma, also known as an acquired digital fibrokeratoma, and acquired periungual fibrokeratoma is a skin lesion characterized by a pinkish, hyperkeratotic, hornlike projection occurring on a finger, toe, or palm.

Congenital onychodysplasia of the index fingers is defined by the presence of the condition at birth, either unilateral or bilateral index finger involvement, variable distortion of the nail or lunula, and polyonychia, micronychia, anonychia, hemi-onychogryphosis, or malalignment.

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Pincer nails are a toenail disorder in which the lateral edges of the nail slowly approach one another, compressing the nailbed and underlying dermis. It occurs less often in the fingernails than toenails, and there usually are no symptoms.

<span class="mw-page-title-main">Preauricular sinus and cyst</span> Medical condition

Preauricular sinuses and preauricular cysts are two common congenital malformations. Each involves the external ear. The difference between them is that a cyst does not connect with the skin, but a sinus does. Frequency of preauricular sinus differs depending the population: 0.1–0.9% in the US, 0.9% in the UK, and 4–10% in Asia and parts of Africa.

References

  1. Tosti, A; Piraccini, BM (2008). "Chapter 70 – Nail Disorders". In Bolognia, JL; Jorizzo, JL; Rapini, RP (eds.). Dermatology. Vol. 1 (2nd ed.). St. Louis: Mosby Elsevier. ISBN   978-1-4160-2999-1.
  2. 1 2 James, William; Berger, Timothy; Elston, Dirk (2005). Andrews' Diseases of the Skin: Clinical Dermatology. (10th ed.). Saunders. ISBN   0-7216-2921-0.
  3. Ram’s horn nails, Dr Nicola Mumoli (cardiologist) - Department of Internal Medicine, Ospedale Civile Livorno, Livorno, Italy, reported in Medical Journal of Australia, MJA 2011; 195 (4): 202, 15 August 2011, accessed 1 September 2011
  4. Johnstone, Ronald B. (2017). "2. Diagnostic clues and "need-to-know" items". Weedon's Skin Pathology Essentials (2nd ed.). Elsevier. p. 31. ISBN   978-0-7020-6830-0.
  5. Freedberg, et al. (2003). Fitzpatrick's Dermatology in General Medicine. (6th ed.). McGraw-Hill. ISBN   0-07-138076-0.
  6. Sequeira JH (1923). "Case of Congenital Onychogryphosis". Proc. R. Soc. Med. 16 (Dermatol Sect): 92. PMC   2103814 . PMID   19982897.
  7. Porteus HB (1954). "A case of onychogryphosis". Br Med J. 2 (4892): 851–2. doi:10.1136/bmj.2.4892.851. PMC   2079501 . PMID   13199328.

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